1. Tau (-)
   1. TDP-43 (+)
      1. FTLD-U with MND
      2. FTLD-U without MND
      3. FTLD-U with PGRN mutation
      4. FTLD-U with VPC mutation
      5. FTLD-U (Ch9)
   2. TDP-43 (-)
      1. Ub (+) with glyosis
         1. FTLD-U with CHMP2B mutation
         2. BIBD
         3. NIFID (alpha-internexin positive)
      2. Ub (-) with glyosis
         1. FTLD (DLDH)
2. Tau (+)
   1. 3 repeat
      1. FTD with Pick body
      2. FTD with MAPT mutation
   2. 4 repeat
      1. CBD
      2. PSP
      3. AGD
      4. FTD with MAPT mutation
   3. 3 + 4 repeat
      1. NFT dementia
      2. FTD with MAPT mutation